Gas-sensing neurons prime mitochondrial fitness to offset metabolic stress (Cornell et al, 2026)

Murph

Senior Member (Voting Rights)
Proc Natl Acad Sci U S A

2026 Mar 10;123(10):e2525619123.
doi: 10.1073/pnas.2525619123. Epub 2026 Mar 4.

Gas-sensing neurons prime mitochondrial fitness to offset metabolic stress​

Rebecca Cornell , Ava Handley, Roger Pocock, Monash University.

Abstract​


The mitochondrial unfolded protein response (UPRmt) is triggered by cells to alleviate proteotoxicity in response to metabolic stress. The ability to anticipate and prime cells against mitochondrial stress, by sensing potentially toxic changes in the external or internal environment, would provide a survival advantage.

Yet, whether and how animals anticipate mitochondrial stress remains unclear. Here, we show that the Caenorhabditis elegans receptor guanylyl cyclase GCY-9 regulates neuropeptide signaling from carbon dioxide-sensing neurons to govern a noncanonical mitochondrial stress response in the intestine.

This noncell autonomous stress response induces atypical mitochondrial chaperone transcription, confers mitochondrial stress resistance, and increases mitochondrial membrane potential and respiration. We show that starvation decreases GCY-9 expression and propose that the resultant cytoprotective program is launched to offset metabolic and proteotoxic risks. Thus, environmental sensing by peripheral neurons can preemptively enhance systemic mitochondrial function in response to metabolic uncertainty.
 
Strengths: big journal, good university, fascinating and possibly useful finding about role of peripheral neurons in controlling mitochondial metabolism. there's a clinical trial going on in mecfs on a guanyl cyclase stimulator, vericiguat.

Weaknesses: research was done on little wee worms.
 
Strengths: big journal, good university, fascinating and possibly useful finding about role of peripheral neurons in controlling mitochondial metabolism. there's a clinical trial going on in mecfs on a guanyl cyclase stimulator, vericiguat.

Weaknesses: research was done on little wee worms.
Is this the trial to which you refer?

https://clinicaltrials.gov/study/NCT05697640

The only two anecdotes from pwME that I was able to locate with a cursory search don't seem to be particularly postive.

 
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